Desmoid tumors are a rare tumor entity seen in about 3-4 cases per 1 million of the population per annum. DT occurs mainly between the age of 15 and 60 years with a peak age of about 30 years.
In Desmoid tumors we have to differentiate between sporadic desmoid tumors and desmoid tumors connected to familial adenomatous polyposis (FAP). Most desmoid tumors occur sporadically only 5-10 percent of all DT arise in the context of FAP. Young adults, especially femals often related to pregnancy are more affected by sporadic DT. In older patients there is no gender preference.